Nuclear huntingtin immunostaining intensity was reduced in Mlh1 +/− striata to approximately 60% of Mlh1 +/+ levels, although this difference did not reach statistical significance (2-tailed unpaired t -test: p = 0.06).
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Mismatch repair genes Mlh1 and Mlh3 modify CAG instability in Huntington's disease mice: genome-wide and candidate approaches.
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