showed a trendp = 0.057
With regard to PPFE severity, patients with extensive PPFE showed a trend towards worse survival (median survival: 6.2 years) than those with limited PPFE (median survival: 8.4 years; p = 0.057) and significantly worse survival than those without PPFE (median survival: 10.4 years; p = 0.029), as shown in Fig. 1 B.